Barnet kellman biography of albert
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Abstract
Never judge a book by its cover, nor assume hypertrophic cardiomyopathy (HCM) as sarcomeric, as appearances can deceive. HCM phenocopies account for a 5–10% of the cases, mainly represented by storage diseases, flagged by the increasing prevalence of senile cardiac amyloid in developing countries. Multisystemic and heterogeneous presentation of these entities is a challenge for clinicians, and time delay in diagnosis is a major concern. Promising drugs and gene-specific tailored therapies are under development, therefore, more than ever, appropriate understanding of these conditions is mandatory for adequate early treatment and counselling.
In this review, storage disorders will be classified as extracellular and intracellular deposit storage diseases, focusing our attention on the most prevalent conditions from the cardiologist’s perspective.
1 Extracellular deposit storage
Cardiac amyloidosis (CA)
Introduction and epidemiology
In the heart, amyloidosis can mimic h
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USC School of Cinematic Arts announces Robin Williams Endowed Chair in Comedy
The George Lucas Family Foundation has established the Robin Williams Endowed Chair in Comedy in honor of the late stand-up comedian and actor, the USC School of Cinematic Arts announced Wednesday.
&#;The immeasurably talented Robin Williams stands as one of the most unique comic voices in entertainment history,&#; said Dean Elizabeth M. Daley. &#;His legendary career, defined by skillful impressions, unforgettable characters and masterful stand-up routines, made him a cherished figure at the forefront of the comedy community. We are so proud to honor his memory and accomplishments at the USC School of Cinematic Arts with the help and generosity of the George Lucas Family Foundation.&#;
Robin was a comedy genius with a boundless talent. &#; His talent was only matched by his work ethic.
George Lucas
George Lucas said: &#;Robin was a comedy genius with a boundless talent. He was singular in every wa
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Gemini
Set in the backyard of a blue-collar South Philadelphia neighborhood early in the summer of , the comedy-drama focuses on the 21st birthday celebration of Harvard lärjunge Francis Geminia Read allSet in the backyard of a blue-collar South Philadelphia neighborhood early in the summer of , the comedy-drama focuses on the 21st birthday celebration of Harvard lärjunge Francis Geminiani. In attendance are his divorced blue collar father Fran and Fran's widowed girlfriend L Read allSet in the backyard of a blue-collar South Philadelphia neighborhood early in the summer of , the comedy-drama focuses on the 21st birthday celebration of Harvard lärling Francis Geminiani. In attendance are his divorced blue collar father Fran and Fran's widowed girlfriend Lucille, next-door neighbor Bunny Weinberger and her overweight son Herschel, and Francis' Read all
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